A challenging case of facial oedemas revealing a systemic peripheral T-cell lymphoma, not otherwise specified
Expert diagnosis and stem cell transplant achieved complete remission in a rare lymphoma masquerading as autoimmune disease.
This case report describes a rare presentation of systemic peripheral T-cell lymphoma (PTCL-NOS) in a young Polynesian patient mimicking autoimmune conditions, ultimately diagnosed via repeated biopsies. Successful treatment with polychemotherapy and allogeneic stem cell transplantation achieved complete remission, underscoring the importance of expert review in challenging lymphoma diagnoses.
What the study was
- Study design
- Single case report
- Population
- Single 20-year-old Polynesian patient
- Sample size
- 1
- Category
- Diagnostics
- Maturity
- Exploratory
- Journal
- European Journal of Dermatology
Why it surfaced
Single case report — capped at triage_score ≤ 4 per protocol; educational value for rare PTCL presentation but not pipeline-critical.
A plain-language summary of published research — not medical advice. Talk to a clinician about your own care.